Activation of peroxisome proliferator-activated receptor pathway stimulates the mitochondrial respiratory chain and can correct deficiencies in patients' cells lacking its components, J Clin Endocrinol Metab, vol.93, pp.1433-1441, 2008. ,
Long-term follow-up of bezafibrate treatment in patients with the myopathic form of carnitine palmitoyltransferase 2 deficiency, 2010. ,
, Clin Pharmacol Ther, vol.88, pp.101-108
Role of peroxisome proliferator-activated receptor-alpha (PPARalpha) in bezafibrateinduced hepatocarcinogenesis and cholestasis, Carcinogenesis, vol.26, pp.219-227, 2005. ,
Bezafibrate at clinically relevant doses decreases serum/liver triglycerides via down-regulation of sterol regulatory element-binding protein-1c in mice: a novel peroxisome proliferator-activated receptor alpha-independent mechanism, Mol Pharmacol, vol.75, pp.782-792, 2009. ,
,
In Vivo Correction of COX Deficiency by Activation of the AMPK/PGC-1alpha Axis, Cell Metab, vol.14, pp.80-90, 2011. ,