E. Gómez-tortosa, A. Del-barrio, G. Ruiz, and P. J. , Severity of cognitive impairment in juvenile and late-onset Huntington disease, Arch Neurol, vol.55, pp.835-843, 1998.

G. Nicolas, D. Devys, and A. Goldenberg, Juvenile Huntington disease in an 18-month-old boy revealed by global developmental delay and reduced cerebellar volume, Am J Med Genet A, vol.155, pp.815-818, 2011.

D. Letort and P. Gonzalez-alegre, Huntington's disease in children, Handb Clin Neurol, vol.113, pp.1913-1917, 2013.

A. Montoya, B. H. Price, and M. Menear, Brain imaging and cognitive dysfunctions in Huntington's disease, J Psychiatry Neurosci, vol.31, pp.21-29, 2006.

V. B. Ho, H. S. Chuang, and M. J. Rovira, Juvenile Huntington disease: CT and MR features, AJNR Am J Neuroradiol, vol.16, pp.1405-1412, 1995.

M. Schapiro, K. M. Cecil, and J. Doescher, MR imaging and spectroscopy in juvenile Huntington disease, Pediatr Radiol, vol.34, pp.640-643, 2004.

C. Fennema-notestine, S. L. Archibald, and M. W. Jacobson, In vivo evidence of cerebellar atrophy and cerebral white matter loss in Huntington disease, Neurology, vol.63, pp.989-995, 2004.

J. Kassubek, W. Gaus, and G. B. Landwehrmeyer, Evidence for more widespread cerebral pathology in early HD: an MRI-based morphometric analysis, Neurology, vol.62, pp.523-524, 2004.

U. Rüb, F. Hoche, and E. R. Brunt, Degeneration of the cerebellum in Huntington's disease (HD): possible relevance for the clinical picture and potential gateway to pathological mechanisms of the disease process, Brain Pathol, vol.23, issue.2, pp.165-177, 2013.

J. Diedrichsen, A spatially unbiased atlas template of the human cerebellum, Neuroimage, vol.33, pp.127-138, 2006.

P. L. Narayanan, C. Warton, R. Boonzaier, and N. , Improved segmentation of cerebellar structures in children, J Neurosci Methods, vol.262, pp.1-13, 2016.

N. K. Focke, S. Trost, and W. Paulus, Do manual and voxelbased morphometry measure the same? A proof of concept study, Front Psychiatry, vol.5, p.39, 2014.

J. V. Manjón and P. Coupé, volBrain: an online MRI brain volumetry system, Front Neuroinform, vol.10, p.30, 2016.

J. E. Romero, P. Coupé, and G. R. , CERES: a new cerebellum lobule segmentation method, Neuroimage, vol.147, pp.916-924, 2017.
URL : https://hal.archives-ouvertes.fr/hal-01398748

J. Ashburner and K. J. Friston, Unified segmentation, Neuroimage, vol.26, pp.839-851, 2005.

S. F. Eskildsen, P. Coupé, and V. Fonov, BEaST: brain extraction based on nonlocal segmentation technique, Neuroimage, vol.59, pp.2362-2373, 2012.
URL : https://hal.archives-ouvertes.fr/inserm-00629187

J. E. Romero, J. V. Manjón, and J. Tohka, NABS: non-local automatic brain hemisphere segmentation, Magn Reson Imaging, vol.33, pp.474-484, 2015.
URL : https://hal.archives-ouvertes.fr/hal-01116696

J. P. Warner, L. H. Barron, and D. J. Brock, A novel gene containing a trinucleotide repeat that is expanded and unstable on Huntington's disease chromosomes. The Huntington's Disease Collaborative Research Group, Mol Cell Probes, vol.7, pp.971-983, 1993.

N. G. Ranen, O. C. Stine, and M. H. Abbott, Anticipation and instability of IT-15 (CAG)n repeats in parent-offspring pairs with Huntington disease, Am J Hum Genet, vol.57, pp.593-602, 1995.

A. D. Moser, E. Epping, P. Espe-pfeifer, M. E. Zhorne, L. Mathews et al., A survey-based study identifies common but unrecognized symptoms in a large series of juvenile Huntington's disease, Neurodegener Dis Manag, vol.7, pp.307-315, 2017.

P. Ribaï, K. Nguyen, and V. Hahn-barma, Psychiatric and cognitive difficulties as indicators of juvenile huntington disease onset in 29 patients, Arch Neurol, vol.64, pp.813-819, 2007.

G. Yoon, J. Kramer, and A. Zanko, Speech and language delay are early manifestations of juvenile-onset Huntington disease, Neurology, vol.67, pp.1265-1267, 2006.

L. J. Cloud, A. Rosenblatt, and R. L. Margolis, Seizures in juvenile Huntington's disease: frequency and characterization in a multicenter cohort, Mov Disord, vol.27, pp.1797-1800, 2012.

N. A. Aziz, J. Van-der-burg, and G. B. Landwehrmeyer, Weight loss in Huntington disease increases with higher CAG repeat number, Neurology, vol.71, pp.1506-1513, 2008.

P. Fusar-poli, J. Radua, and M. Frascarelli, Evidence of reporting biases in voxel-based morphometry (VBM) studies of psychiatric and neurological disorders, Hum Brain Mapp, vol.35, pp.3052-3065, 2014.

S. Kühn, A. Romanowski, and F. Schubert, Reduction of cerebellar grey matter in Crus I and II in schizophrenia, Brain Struct Funct, vol.217, pp.523-529, 2012.

G. J. Harris, G. D. Pearlson, and C. E. Peyser, Putamen volume reduction on magnetic resonance imaging exceeds caudate changes in mild Huntington's disease, Ann Neurol, vol.31, pp.69-75, 1992.

E. H. Aylward, J. Brandt, and A. M. Codori, Reduced basal ganglia volume associated with the gene for Huntington's disease in asymptomatic at-risk persons, Neurology, vol.44, pp.823-828, 1994.

J. P. Aggleton and M. Mishkin, The amygdala: Sensory gateway to the emotions, Biological foundations of emotion, pp.281-299, 1986.

A. K. Anderson and E. A. Phelps, Lesions of the human amygdala impair enhanced perception of emotionally salient events, Nature, vol.411, pp.305-309, 2001.

K. W. Lange, B. J. Sahakian, and N. P. Quinn, Comparison of executive and visuospatial memory function in Huntington's disease and dementia of Alzheimer type matched for degree of dementia, J Neurol Neurosurg Psychiatry, vol.58, pp.598-606, 1995.

A. D. Lawrence, B. J. Sahakian, and J. R. Hodges, Executive and mnemonic functions in early Huntington's disease, Brain J Neurol, vol.119, pp.1633-1645, 1996.

E. Bollen, J. P. Reulen, D. Heyer, and J. C. , Horizontal and vertical saccadic eye movement abnormalities in Huntington's chorea, J Neurol Sci, vol.74, pp.11-22, 1986.

P. Hansotia, R. Wall, and J. Berendes, Sleep disturbances and severity of Huntington's disease, Neurology, vol.35, pp.1672-1674, 1985.

D. V. Jeste, L. Barban, and J. Parisi, Reduced Purkinje cell density in Huntington's disease, Exp Neurol, vol.85, pp.78-86, 1984.

R. A. Rodda, Cerebellar atrophy in Huntington's disease, J Neurol Sci, vol.50, pp.147-157, 1981.

P. Vinken and G. Bruyn, Extrapyramidal disorders. Elsevier Science Health Science Division, 1987.

H. D. Rosas, W. J. Koroshetz, and Y. I. Chen, Evidence for more widespread cerebral pathology in early HD: an MRI-based morphometric analysis, Neurology, vol.60, pp.1615-1620, 2003.

J. P. Vonsattel and M. Difiglia, J Neuropathol Exp Neurol, vol.57, pp.369-384, 1998.

J. P. Vonsattel, R. H. Myers, and T. J. Stevens, Neuropathological classification of Huntington's disease, J Neuropathol Exp Neurol, vol.44, pp.559-577, 1985.

E. M. Rees, R. Farmer, and J. H. Cole, Cerebellar abnormalities in Huntington's disease: a role in motor and psychiatric impairment?, Mov Disord, vol.29, pp.1648-1654, 2014.

P. S. Harper, Huntington's disease. WB Saunders, pp.1-15, 1991.

G. A. Jervis, Huntington's chorea in childhood, Arch Neurol, vol.9, pp.244-257, 1963.

C. H. Markham and J. W. Knox, Observations on Huntington's chorea in childhood, J Pediatr, vol.67, pp.46-57, 1965.

R. K. Byers, F. H. Gilles, and C. Fung, Huntington's disease in children. Neuropathologic study of four cases, Neurology, vol.23, pp.561-569, 1973.

J. Vonsattel, C. Keller, C. Ramirez, and E. P. , Huntington's disease -neuropathology, Handb Clin Neurol, vol.100, pp.83-100, 2011.

A. Rasmussen, R. Macias, and P. Yescas, Huntington disease in children: genotype-phenotype correlation, Neuropediatrics, vol.31, pp.190-194, 2000.

M. Gencik, C. Hammans, and H. Strehl, Chorea Huntington: a rare case with childhood onset, Neuropediatrics, vol.33, pp.90-92, 2002.

J. M. Milunsky, T. A. Maher, and B. A. Loose, XL PCR for the detection of large trinucleotide expansions in juvenile Huntington's disease, Clin Genet, vol.64, pp.70-73, 2003.

F. A. Nahhas, J. Garbern, and K. M. Krajewski, Juvenile onset Huntington disease resulting from a very large maternal expansion, Am J Med Genet A, vol.137, pp.328-331, 2005.

S. Seneca, D. Fagnart, and K. Keymolen, Early onset Huntington disease: a neuronal degeneration syndrome, Eur J Pediatr, vol.163, pp.717-721, 2004.

S. Sakazume, S. Yoshinari, and E. Oguma, A patient with early onset Huntington disease and severe cerebellar atrophy, Am J Med Genet A, vol.149, pp.598-601, 2009.

I. Fyfe, Dementia: cerebellar atrophy has disease-specific patterns, Nat Rev Neurol, vol.12, p.188, 2016.

R. Crooks, T. Mitchell, and M. Thom, Patterns of cerebellar atrophy in patients with chronic epilepsy: a quantitative neuropathological study, Epilepsy Res, vol.41, pp.63-73, 2000.

G. Hagemann, L. Lemieux, and S. L. Free, Cerebellar volumes in newly diagnosed and chronic epilepsy, J Neurol, vol.249, pp.1651-1658, 2002.

C. C. Guo, R. Tan, and J. R. Hodges, Network-selective vulnerability of the human cerebellum to Alzheimer's disease and frontotemporal dementia, Brain J Neurol, vol.139, pp.1527-1538, 2016.

A. W. Deckel, Is Huntington's disease of cerebellar/brainstem origin?, Lancet, vol.345, pp.263-264, 1995.

F. Squitieri, G. Pustorino, and M. Cannella, Highly disabling cerebellar presentation in Huntington disease, Eur J Neurol, vol.10, pp.443-444, 2003.