S. Cronin, O. Hardiman, and B. Trayno, Ethnic variation in the incidence of ALS: A systematic review, Neurology, vol.68, issue.13, pp.1002-1009, 2007.
DOI : 10.1212/01.wnl.0000258551.96893.6f

J. Curtis and R. Burt, Point: The Ethics of Unilateral ???Do Not Resuscitate??? Orders, Chest, vol.132, issue.3, pp.748-51, 2007.
DOI : 10.1378/chest.07-0745

E. Emmanuel and L. Emmanuel, Four Models of the Physician-Patient Relationship, JAMA: The Journal of the American Medical Association, vol.267, issue.16, pp.2221-2227, 1992.
DOI : 10.1001/jama.1992.03480160079038

A. Gauthier, A. Vignola, and A. Calvo, A longitudinal study on quality of life and depression in ALS patient???caregiver couples, Neurology, vol.68, issue.12, pp.923-929, 2007.
DOI : 10.1212/01.wnl.0000257093.53430.a8

M. Geoffroy, D. Blet, and A. Boch, Aide a ` la ré flexion face aux situations extrê mes, Ethique Sante, vol.4, pp.165-173, 2007.

M. Guerrier, Quels sont les aspects e ´ thiques des dé cisions de supplé ance et de leur ré versibilité ? Texte du groupe bibliographique de la confé rence de consensus sur la « prise en charge des personnes atteintes de sclé rose laté rale amyotrophique, Rev Neurol (Paris), vol.62, pp.4-334, 2006.

H. Hayashi and E. Oppenheimer, ALS patients on TPPV: Totally locked-in state, neurologic findings and ethical implications, Neurology, vol.61, issue.1, pp.135-142, 2003.
DOI : 10.1212/01.WNL.0000069925.02052.1F

R. Mandler, A. Jr, F. Miller, and R. , The ALS Patient Care Database: Insights into End-of-Life Care in ALS, Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders, vol.2, issue.4, pp.203-211, 2001.
DOI : 10.1080/14660820152882214

C. Manthous, Counterpoint: Is It Ethical To Order ???Do Not Resuscitate??? Without Patient Consent?, Chest, vol.132, issue.3, pp.51-55, 2007.
DOI : 10.1378/chest.07-0912

A. Millul, E. Beghi, G. Logroscino, A. Micheli, E. Vitelli et al., Survival of Patients with Amyotrophic Lateral Sclerosis in a Population-Based Registry, Neuroepidemiology, vol.25, issue.3, pp.114-123, 2005.
DOI : 10.1159/000086353

R. Morgan, S. Mcnally, and A. M. , Use of Sniff Nasal-Inspiratory Force to Predict Survival in Amyotrophic Lateral Sclerosis, American Journal of Respiratory and Critical Care Medicine, vol.171, issue.3, pp.269-74, 2005.
DOI : 10.1164/rccm.200403-314OC

C. Munroe, M. Sirdofsky, T. Kuru, and E. Anderson, End-of-life decision making in 42 patients with amyotrophic lateral sclerosis, Respir Care, vol.52, pp.996-1005, 2007.

O. 'toole, O. Traynor, B. Brennan, P. Sheehan, C. Frost et al., Epidemiology and clinical features of amyotrophic lateral sclerosis in Ireland between 1995 and 2004, Journal of Neurology, Neurosurgery & Psychiatry, vol.79, issue.1, pp.30-32, 1995.
DOI : 10.1136/jnnp.2007.117788

J. Rabkin, S. Albert, T. Tider, D. Bene, M. et al., Predictors and course of elective long???term mechanical ventilation: A prospective study of ALS patients, Amyotrophic Lateral Sclerosis, vol.169, issue.1, pp.86-95, 2006.
DOI : 10.1159/000086679

H. Schreiber, T. Gaigalat, U. Wiedemuth-catrinescu, M. Graf, I. Uttner et al., Cognitive function in bulbar??? and spinal???onset amyotrophic lateral sclerosis, Journal of Neurology, vol.57, issue.7, pp.772-81, 2005.
DOI : 10.1007/s00415-005-0739-6

M. Silverstein, C. Stocking, J. Antel, J. Beckwith, R. Roos et al., Amyotrophic Lateral Sclerosis and Life-Sustaining Therapy: Patients' Desires for Information, Participation in Decision Making, and Life-Sustaining Therapy, Mayo Clinic Proceedings, vol.66, issue.9, pp.906-919, 1991.
DOI : 10.1016/S0025-6196(12)61577-8

A. Smyth, M. Riedl, R. Kimura, R. Olick, and M. Siegler, End of life decisions in amyotrophic lateral sclerosis: a cross-cultural perspective, Journal of the Neurological Sciences, vol.152, pp.93-99, 1997.
DOI : 10.1016/S0022-510X(97)00253-0

P. Terrry, Informed Consent in Clinical Medicine, Chest, vol.131, issue.2, pp.563-571, 2007.
DOI : 10.1378/chest.06-1955

F. Torny, M. Lacoste, J. Nguyen, M. Tymoczko-nguyen, and P. Couratier, ??tude des causes du retard au diagnostic de la scl??rose lat??rale amyotrophique, Revue Neurologique, vol.162, issue.5, pp.617-639, 2006.
DOI : 10.1016/S0035-3787(06)75055-X