J. Gil, B. Funalot, A. Verschueren, V. Danel-brunaud, W. Camu et al., Causes of death amongst French patients with amyotrophic lateral sclerosis: a prospective study, European Journal of Neurology, vol.298, issue.Suppl. 1, pp.1245-1251, 2008.
DOI : 10.1111/j.1468-1331.2008.02307.x

S. Bourke, M. Tomlinson, T. Williams, R. Bullock, P. Shaw et al., Effects of non-invasive ventilation on survival and quality of life in patients with amyotrophic lateral sclerosis: a randomised controlled trial, The Lancet Neurology, vol.5, issue.2, pp.140-147, 2006.
DOI : 10.1016/S1474-4422(05)70326-4

T. Similowski, V. Attali, G. Bensimon, F. Salachas, S. Mehiri et al., Diaphragmatic dysfunction and dyspnoea in amyotrophic lateral sclerosis, European Respiratory Journal, vol.15, issue.2, pp.332-337, 2000.
DOI : 10.1034/j.1399-3003.2000.15b19.x

I. Arnulf, T. Similowski, F. Salachas, L. Garma, S. Mehiri et al., Sleep Disorders and Diaphragmatic Function in Patients with Amyotrophic Lateral Sclerosis, American Journal of Respiratory and Critical Care Medicine, vol.161, issue.3, pp.849-856, 2000.
DOI : 10.1164/ajrccm.161.3.9805008

C. Bouteloup, J. Desport, P. Clavelou, N. Guy, H. Derumeaux-burel et al., Hypermetabolism in ALS patients: an early and persistent phenomenon, Journal of Neurology, vol.156, issue.suppl. 2, pp.1236-1242, 2009.
DOI : 10.1007/s00415-009-5100-z
URL : https://hal.archives-ouvertes.fr/hal-00406539

J. Desport, P. Preux, L. Magy, Y. Boirie, J. Vallat et al., Factors correlated with hypermetabolism in patients with amyotrophic lateral sclerosis, Am J Clin Nutr, vol.74, pp.328-334, 2001.

J. Desport, F. Torny, M. Lacoste, P. Preux, and P. Couratier, Hypermetabolism in ALS: Correlations with Clinical and Paraclinical Parameters, Neurodegenerative Diseases, vol.2, issue.3-4, pp.202-207, 2005.
DOI : 10.1159/000089626

T. Shimizu, U. Nagaoka, Y. Nakayama, A. Kawata, C. Kugimoto et al., Reduction rate of body mass index predicts prognosis for survival in amyotrophic lateral sclerosis: A multicenter study in Japan, Amyotrophic Lateral Sclerosis, vol.73, issue.4, pp.363-366, 2012.
DOI : 10.1016/j.clnu.2009.06.002

P. Clavelou, M. Blanquet, F. Peyrol, L. Ouchchane, and L. Gerbaud, Rates of progression of weight and forced vital capacity as relevant measurement to adapt Amyotrophic Lateral Sclerosis management for patient Result of a French multicentre cohort survey, Journal of the Neurological Sciences, vol.331, issue.1-2, pp.126-131, 2013.
DOI : 10.1016/j.jns.2013.06.002

S. Korner, M. Hendricks, K. Kollewe, A. Zapf, R. Dengler et al., Weight loss, dysphagia and supplement intake in patients with amyotrophic lateral sclerosis (ALS): impact on quality of life and therapeutic options, BMC Neurology, vol.31, issue.Suppl 2, p.84, 2013.
DOI : 10.1080/14660820310011728

V. Attali, S. Mehiri, C. Straus, F. Salachas, I. Arnulf et al., Influence of Neck Muscles on Mouth Pressure Response to Cervical Magnetic Stimulation, American Journal of Respiratory and Critical Care Medicine, vol.156, issue.2, pp.509-514, 1997.
DOI : 10.1164/ajrccm.156.2.9612053

B. Brooks, R. Miller, M. Swash, and T. Munsat, El Escorial revisited: Revised criteria for the diagnosis of amyotrophic lateral sclerosis, Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders, vol.1, issue.5, pp.293-299, 2000.
DOI : 10.1080/146608200300079536

P. Andersen, G. Borasio, R. Dengler, O. Hardiman, K. Kollewe et al., EFNS task force on management of amyotrophic lateral sclerosis: guidelines for diagnosing and clinical care of patients and relatives. An evidence-based review with good practice points, European Journal of Neurology, vol.58, issue.5, pp.921-938, 2005.
DOI : 10.1136/jnnp.70.3.417

J. Gonzalez-bermejo, C. Morelot-panzini, N. Arnol, V. Meininger, S. Kraoua et al., Prognostic value of efficiently correcting nocturnal desaturations after one month of non-invasive ventilation in amyotrophic lateral sclerosis: A retrospective monocentre observational cohort study, Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration, vol.81, issue.5-6, pp.373-379, 2013.
DOI : 10.1164/rccm.200307-885ST

J. Gonzalez-bermejo, C. Perrin, J. Janssens, J. Pepin, G. Mroue et al., Proposal for a systematic analysis of polygraphy or polysomnography for identifying and scoring abnormal events occurring during non-invasive ventilation, Thorax, vol.67, issue.6, pp.546-552, 2012.
DOI : 10.1136/thx.2010.142653

J. Harris and F. Benedict, A Biometric Study of Human Basal Metabolism, Proceedings of the National Academy of Sciences, vol.4, issue.12, pp.370-373, 1918.
DOI : 10.1073/pnas.4.12.370

M. Sundstrom, I. Tjader, O. Rooyackers, and J. Wernerman, Indirect calorimetry in mechanically ventilated patients. A systematic comparison of three instruments, Clinical Nutrition, vol.32, issue.1, pp.118-121, 2013.
DOI : 10.1016/j.clnu.2012.06.004

A. Cournand, D. Richards, . Jr, R. Bader, M. Bader et al., The oxygen cost of breathing, Trans Assoc Am Phys, vol.67, pp.162-173, 1954.

J. Silver, The oxygen cost of breathing in tetraplegic patients, Paraplegia, vol.1, issue.3, pp.204-214, 1963.
DOI : 10.1172/JCI103663

R. Bartlett, . Jr, H. Brubach, and H. Specht, Oxygen cost of breathing, JApplPhysiol, vol.12, pp.413-424, 1958.

E. Campbell, E. Westlake, and R. Cherniack, Simple methods of estimating oxygen consumption and efficiency of the muscles of breathing, pp.303-308, 1957.

D. Dodd, J. Yarom, S. Loring, and L. Engel, O2 cost of inspiratory and expiratory resistive breathing in humans, pp.2518-2523, 1988.

R. Margaria, G. Milic-emili, J. Petit, and G. Cavagna, Mechanical work of breathing during muscular exercise, J Appl Physiol, vol.15, pp.354-358, 1960.

H. Manning, F. Mccool, S. Scharf, E. Garshick, and R. Brown, Oxygen cost of resistive-loaded breathing in quadriplegia, pp.825-831, 1992.

G. Liljestrand, Untersechungen uber die atmungsarbeit. Scan Arch Physiol, pp.199-293, 1918.

N. Thung, P. Herzog, I. Christlieb, W. Thompson, . Jr et al., THE COST OF RESPIRATORY EFFORT IN POSTOPERATIVE CARDIAC PATIENTS, Survey of Anesthesiology, vol.8, issue.6, pp.552-559, 1963.
DOI : 10.1097/00132586-196412000-00042

R. Wilson, S. Sullivan, J. Malm, F. Bowman, and . Jr, The Oxygen Cost of Breathing Following Anesthesia and Cardiac Surgery, Anesthesiology, vol.39, issue.4, pp.387-393, 1973.
DOI : 10.1097/00000542-197310000-00008

O. Hugli, Y. Schutz, and J. Fitting, The Cost of Breathing in Stable Chronic Obstructive Pulmonary Disease, Clinical Science, vol.89, issue.6, pp.625-632, 1995.
DOI : 10.1042/cs0890625

J. Gonzalez-bermejo, . Morelot-panzinic, and D. Georgesm, Can diaphragm pacing improve gas exchange? Insights from quadriplegic patients, European Respiratory Journal, vol.43, issue.1, pp.303-306, 2014.
DOI : 10.1183/09031936.00127713

H. Barle, P. Soderberg, C. Haegerstrand, and A. Markstrom, Bi-level positive airway pressure ventilation reduces the oxygen cost of breathing in long-standing post-polio patients on invasive home mechanical ventilation, Acta Anaesthesiologica Scandinavica, vol.134, issue.2, pp.197-202, 2005.
DOI : 10.1054/clnu.2001.0473

M. Sherman, A. Pillai, A. Jackson, and T. Heiman-patterson, Standard Equations Are Not Accurate in Assessing Resting Energy Expenditure in Patients With Amyotrophic Lateral Sclerosis, Journal of Parenteral and Enteral Nutrition, vol.28, issue.6, pp.442-446, 2004.
DOI : 10.1177/0148607104028006442

A. Ellis and J. Rosenfeld, Which Equation Best Predicts Energy Expenditure in Amyotrophic Lateral Sclerosis?, Journal of the American Dietetic Association, vol.111, issue.11, pp.1680-1687, 2011.
DOI : 10.1016/j.jada.2011.08.002

P. Weijs, Hypermetabolism, Is It Real? The Example of Amyotrophic Lateral Sclerosis, Journal of the American Dietetic Association, vol.111, issue.11, pp.1670-1673, 2011.
DOI : 10.1016/j.jada.2011.08.011

E. Kasarskis, S. Berryman, J. Vanderleest, A. Schneider, and C. Mcclain, Nutritional status of patients with amyotrophic lateral sclerosis: relation to the proximity of death, Am J Clin Nutr, vol.63, pp.130-137, 1996.

N. Vaisman, M. Lusaus, B. Nefussy, E. Niv, D. Comaneshter et al., Do patients with amyotrophic lateral sclerosis (ALS) have increased energy needs?, Journal of the Neurological Sciences, vol.279, issue.1-2, pp.26-29, 2009.
DOI : 10.1016/j.jns.2008.12.027

J. Hoit, R. Lansing, K. Dean, M. Yarkosky, and A. Lederle, Nature and Evaluation of Dyspnea in Speaking and Swallowing, Seminars in Speech and Language, vol.32, issue.01, pp.5-20, 2011.
DOI : 10.1055/s-0031-1271971

A. Schols, R. Mostert, N. Cobben, P. Soeters, and E. Wouters, Transcutaneous Oxygen Saturation and Carbon Dioxide Tension during Meals in Patients with Chronic Obstructive Pulmonary Disease, Chest, vol.100, issue.5, pp.1287-1292, 1991.
DOI : 10.1378/chest.100.5.1287

N. Wolkove, L. Fu, A. Purohit, A. Colacone, and H. Kreisman, Meal Induced Oxygen Desaturation and Dyspnea in Chronic Obstructive Pulmonary Disease, Canadian Respiratory Journal, vol.5, issue.5, pp.361-365, 1998.
DOI : 10.1155/1998/347020

W. Siirala, K. Olkkola, T. Noponen, A. Vuori, and R. Aantaa, Predictive equations over-estimate the resting energy expenditure in amyotrophic lateral sclerosis patients who are dependent on invasive ventilation support, Nutrition & Metabolism, vol.7, issue.1, p.70, 2010.
DOI : 10.1186/1743-7075-7-70

J. Gonzalez-bermejo, F. Lofaso, L. Falaize, M. Lejaille, J. Raphael et al., Resting energy expenditure in Duchenne patients using home mechanical ventilation, European Respiratory Journal, vol.25, issue.4, pp.682-687, 2005.
DOI : 10.1183/09031936.05.00031304

N. Lechtzin, Y. Scott, A. Busse, L. Clawson, R. Kimball et al., Early use of non???invasive ventilation prolongs survival in subjects with ALS, Amyotrophic Lateral Sclerosis, vol.163, issue.3, pp.185-188, 2007.
DOI : 10.1080/146608200300079536

L. Leonardis, D. Groselj, L. Vidmar, and G. , Factors related to respiration influencing survival and respiratory function in patients with amyotrophic lateral sclerosis: a retrospective study, European Journal of Neurology, vol.127, issue.Suppl, pp.1518-1524, 2012.
DOI : 10.1111/j.1468-1331.2012.03754.x

. Georges, Noninvasive ventilation reduces energy expenditure in amyotrophic lateral sclerosis, BMC Pulmonary Medicine, vol.19, issue.1, p.17, 2014.
DOI : 10.1111/j.1468-1331.2012.03754.x
URL : https://hal.archives-ouvertes.fr/inserm-00945682