Separating Fact from Fiction: Assessing the Potential of Modified Adenovirus Vectors for Use in Human Gene Therapy, Current Gene Therapy, vol.2, issue.2, pp.111-133, 2002. ,
DOI : 10.2174/1566523024605618
Histological parameters for the quantitative assessment of muscular dystrophy in the mdx-mouse, Neuromuscular Disorders, vol.14, issue.10, pp.675-682, 2004. ,
DOI : 10.1016/j.nmd.2004.06.008
Stimulation of calcineurin signaling attenuates the dystrophic pathology in mdx mice, Human Molecular Genetics, vol.13, issue.4, pp.379-388, 2004. ,
DOI : 10.1093/hmg/ddh037
Molecular, cellular, and pharmacological therapies for Duchenne/Becker muscular dystrophies, The FASEB Journal, vol.19, issue.8, pp.880-891, 2005. ,
DOI : 10.1096/fj.04-1956rev
A barometric method for measuring ventilation in newborn infants, Pediatrics, vol.16, pp.81-87, 1955. ,
Voluntary exercise decreases progression of muscular dystrophy in diaphragm of mdx mice, J Appl Physiol, vol.77, pp.1736-1741, 1994. ,
Exercise and clenbuterol as strategies to decrease the progression of muscular dystrophy in mdx mice, J Appl Physiol, vol.80, pp.734-741, 1996. ,
Differential expression of muscular dystrophy in diaphragm versus hindlimb muscles of mdx mice, Muscle & Nerve, vol.333, issue.10, pp.1105-1110, 1992. ,
DOI : 10.1002/mus.880151008
Long-term benefit from prednisone therapy in Duchenne muscular dystrophy, Neurology, vol.41, issue.12, pp.1874-1877, 1991. ,
DOI : 10.1212/WNL.41.12.1874
A beneficial effect of oxandrolone in the treatment of Duchenne muscular dystrophy: A pilot study, Neurology, vol.48, issue.5, pp.1225-1226, 1997. ,
DOI : 10.1212/WNL.48.5.1225
Ventilatory dysfunction inmdx mice: Impact of tumor necrosis factor-alpha deletion, Muscle & Nerve, vol.153, issue.3, pp.336-343, 2003. ,
DOI : 10.1002/mus.10431
Rescue of Dystrophic Muscle Through U7 snRNA-Mediated Exon Skipping, Science, vol.306, issue.5702, pp.1796-1799, 2004. ,
DOI : 10.1126/science.1104297
Dystrophin expression in the mdx mouse restored by stem cell transplantation, Nature, vol.14, issue.6751, pp.390-394, 1999. ,
DOI : 10.1038/43919
Clinical implications of maximal respiratory pressure determinations for individuals with duchenne muscular dystrophy, Archives of Physical Medicine and Rehabilitation, vol.78, issue.1, pp.1-6, 1997. ,
DOI : 10.1016/S0003-9993(97)90001-0
Noninvasive Measurement of Airway Responsiveness in Allergic Mice Using Barometric Plethysmography, American Journal of Respiratory and Critical Care Medicine, vol.156, issue.3, pp.766-775, 1997. ,
DOI : 10.1164/ajrccm.156.3.9606031
Progression of kyphosis in mdx mice, Journal of Applied Physiology, vol.97, issue.5, pp.1970-1977, 2004. ,
DOI : 10.1152/japplphysiol.01357.2003
Phenotype of dystrophinopathy in oldMDX mice, The Anatomical Record, vol.14, issue.1, pp.70-76, 1995. ,
DOI : 10.1002/ar.1092420109
Morphometric analysis of mdx diaphragm muscle fibres. Comparison with hindlimb muscles, Neuromuscular Disorders, vol.3, issue.5-6, pp.463-469, 1993. ,
DOI : 10.1016/0960-8966(93)90098-5
Contractile properties of diaphragm muscle segments from old mdx and old transgenic mdx mice, Am J Physiol, vol.272, pp.2063-2068, 1997. ,
mice 6-28 months old, The Journal of Physiology, vol.104, issue.2, pp.591-600, 2001. ,
DOI : 10.1111/j.1469-7793.2001.00591.x
A standardized method for the evaluation of respiratory muscle endurance in patients with Duchenne muscular dystrophy, Neuromuscular Disorders, vol.11, issue.2, pp.171-177, 2001. ,
DOI : 10.1016/S0960-8966(00)00179-6
The effect of respiratory muscle training with CO2 breathing on cellular adaptation of mdx mouse diaphragm, Neuromuscular Disorders, vol.15, issue.6, pp.427-436, 2005. ,
DOI : 10.1016/j.nmd.2005.01.014
URL : https://hal.archives-ouvertes.fr/inserm-00149357
Myoblast Transfer in the Treatment of Duchenne's Muscular Dystrophy, New England Journal of Medicine, vol.333, issue.13, pp.832-838, 1995. ,
DOI : 10.1056/NEJM199509283331303
Myoblast transfer therapy: is there any light at the end of the tunnel?, Acta Myol, vol.24, pp.128-133, 2005. ,
Translocation (X; Y) and genetic counseling], J Genet Hum, vol.36, pp.93-97, 1988. ,
mdx mice show progressive weakness and muscle deterioration with age, Journal of the Neurological Sciences, vol.129, issue.2, pp.97-105, 1995. ,
DOI : 10.1016/0022-510X(94)00276-T
Adaptations in myosin heavy chain expression and contractile function in dystrophic mouse diaphragm, Am J Physiol, vol.265, pp.834-841, 1993. ,
Gentamicin administration in Duchenne patients with premature stop codon. Preliminary results, Acta Myol, vol.22, pp.15-21, 2003. ,
Duchenne muscular dystrophy: Focus on pharmaceutical and nutritional interventions, The International Journal of Biochemistry & Cell Biology, vol.39, issue.3, pp.469-477, 2007. ,
DOI : 10.1016/j.biocel.2006.09.009
The molecular basis of muscular dystrophy in the mdx mouse: a point mutation, Science, vol.244, issue.4912, pp.1578-1580, 1989. ,
DOI : 10.1126/science.2662404
Progress in myoblast transplantation: a potential treatment of dystrophies, Microscopy Research and Technique, vol.105, issue.2, pp.213-222, 2000. ,
DOI : 10.1002/(SICI)1097-0029(20000201/15)48:3/4<213::AID-JEMT9>3.0.CO;2-Z
The mdx mouse diaphragm reproduces the degenerative changes of Duchenne muscular dystrophy, Nature, vol.352, issue.6335, pp.536-539, 1991. ,
DOI : 10.1038/352536a0
Hypercapnic ventilatory responses in mice differentially susceptible to acute ozone exposure, J Appl Physiol, vol.75, pp.2613-2619, 1993. ,
Genetic control of differential baseline breathing pattern, J Appl Physiol, vol.82, pp.874-881, 1997. ,
Creatine monohydrate enhances strength and body composition in Duchenne muscular dystrophy, Neurology, vol.62, issue.10, pp.1771-1777, 2004. ,
DOI : 10.1212/01.WNL.0000125178.18862.9D
-arginine improves dystrophic phenotype in mice, Neurobiology of Disease, vol.20, issue.1, pp.123-130, 2005. ,
DOI : 10.1016/j.nbd.2005.02.010
URL : https://hal.archives-ouvertes.fr/in2p3-01009308
Inspiratory Muscle Training in Patients With Duchenne Muscular Dystrophy, Chest, vol.105, issue.2, pp.475-482, 1994. ,
DOI : 10.1378/chest.105.2.475
Long-term persistence of plasmid DNA and foreign gone expression in mouse muscle, Human Molecular Genetics, vol.1, issue.6, pp.363-369, 1992. ,
DOI : 10.1093/hmg/1.6.363
Long-term electrical stimulation of muscles in children with duchenne and becker muscular dystrophy, Muscle & Nerve, vol.44, issue.3, pp.362-367, 1992. ,
DOI : 10.1002/mus.880150316