K. Ekberg, B. Landau, and A. Wajngot, Contributions by kidney and liver to glucose production in the postabsorptive state and after 60 h of fasting, Diabetes, vol.48, issue.2, pp.292-298, 1999.
DOI : 10.2337/diabetes.48.2.292

M. Emmett and R. Narins, Renal tranplantation in type 1 glycogenosis. Failure to improve glucose metabolism, JAMA: The Journal of the American Medical Association, vol.239, issue.16, pp.1642-1644, 1978.
DOI : 10.1001/jama.239.16.1642

L. Faivre, D. Houssin, and J. Valayer, Long-term outcome of liver transplantation in patients with glycogen storage disease type Ia, Journal of Inherited Metabolic Disease, vol.22, issue.6, pp.723-732, 1999.
DOI : 10.1023/A:1005544117285

J. Field, S. Epstein, T. Egan, R. Fine, M. Kogut et al., Studies in Glycogen Storage Diseases. I. Intestinal Glucose-6-Phosphatase Activity in Patients with Von Gierke's Disease and Their Parents*, Journal of Clinical Investigation, vol.44, issue.7, pp.1240-1247632, 1965.
DOI : 10.1172/JCI105230

L. Franco, V. Krishnamurthy, and D. Bali, Hepatocellular carcinoma in glycogen storage disease type Ia: A case series, Journal of Inherited Metabolic Disease, vol.28, issue.2, pp.153-162, 2005.
DOI : 10.1007/s10545-005-7500-2

J. Gerich, C. Meyer, H. Woerle, and M. Stumvoll, Renal Gluconeogenesis: Its importance in human glucose homeostasis, Diabetes Care, vol.24, issue.2, pp.382-391, 2001.
DOI : 10.2337/diacare.24.2.382

A. Ghosh, M. Allamarvdasht, and C. Pan, Long-term correction of murine glycogen storage disease type Ia by recombinant adeno-associated virus-1-mediated gene transfer, Gene Therapy, vol.14, issue.4, pp.321-329, 2006.
DOI : 10.1038/sj.gt.3301068

J. Girard, P. Ferré, J. Pégorier, and P. Duée, Adaptations of glucose and fatty acid metabolism during perinatal period and suckling-weaning transition, Physiol Rev, vol.72, pp.507-562, 1992.

S. Heller, L. Worona, and C. A. , Nutritional Therapy for Glycogen Storage Diseases, Journal of Pediatric Gastroenterology and Nutrition, vol.47, issue.Suppl 1, p.47, 2008.
DOI : 10.1097/MPG.0b013e3181818ea5

S. Kim, D. Weinstein, and M. Starost, Necrotic foci, elevated chemokines and infiltrating neutrophils in the liver of glycogen storage disease type Ia, Journal of Hepatology, vol.48, issue.3, pp.479-485, 2008.
DOI : 10.1016/j.jhep.2007.11.014

P. Kishnani, Y. Bao, and J. Wu, Isolation and Nucleotide Sequence of Canine Glucose-6-phosphatase mRNA: Identification of Mutation in Puppies with Glycogen Storage Disease Type Ia, Biochemical and Molecular Medicine, vol.61, issue.2, pp.168-177, 1997.
DOI : 10.1006/bmme.1997.2600

P. Kishnani, E. Faulkner, and S. Vancamp, Canine Model and Genomic Structural Organization of Glycogen Storage Disease Type Ia (GSD Ia), Veterinary Pathology, vol.275, issue.1, pp.83-91, 2001.
DOI : 10.1354/vp.38-1-83

P. Labrune, K. Lei, H. Chen, and C. Pan, Glycogen storage disease type I: indications for liver and/or kidney transplantation, European Journal of Pediatrics, vol.137, issue.Suppl 1, pp.53-55, 1038.
DOI : 10.1007/BF02679995

X. Luo, G. Hall, and S. Li, Hepatorenal Correction in Murine Glycogen Storage Disease Type I With a Double-stranded Adeno-associated Virus Vector, Molecular Therapy, vol.19, issue.11, pp.1961-1970, 2011.
DOI : 10.1038/mt.2011.126

D. Martens, J. Rake, and G. Navis, Renal Function in Glycogen Storage Disease Type I, Natural Course, and Renopreservative Effects of ACE Inhibition, Clinical Journal of the American Society of Nephrology, vol.4, issue.11, pp.1741-1746, 2009.
DOI : 10.2215/CJN.00050109

P. Milla, D. Atherton, and J. Leonard, Disordered intestinal function in glycogen storage disease, Journal of Inherited Metabolic Disease, vol.8, issue.4, pp.155-157, 1978.
DOI : 10.1007/BF01805585

R. Santer, G. Hillebrand, B. Steinmann, and J. Schaub, Intestinal glucose transport: Evidence for a membrane traffic???based pathway in humans, Gastroenterology, vol.124, issue.1, pp.34-39, 2003.
DOI : 10.1053/gast.2003.50009

M. Soty, J. Chilloux, and S. Casteras, New insights into the organisation and intracellular localisation of the two subunits of glucose-6-phosphatase, Biochimie, vol.94, issue.3, pp.695-703, 2012.
DOI : 10.1016/j.biochi.2011.09.022

URL : https://hal.archives-ouvertes.fr/inserm-00737760

F. Stümpel, R. Burcelin, K. Jungermann, and B. Thorens, Normal kinetics of intestinal glucose absorption in the absence of GLUT2: Evidence for a transport pathway requiring glucose phosphorylation and transfer into the endoplasmic reticulum, Proceedings of the National Academy of Sciences, vol.98, issue.20, pp.11330-11335, 2001.
DOI : 10.1073/pnas.211357698

G. Visser, J. Rake, and F. Kokke, Intestinal function in glycogen storage disease type I, Journal of Inherited Metabolic Disease, vol.25, issue.4, pp.261-267, 2002.
DOI : 10.1023/A:1016572706488

D. Wang, L. Fiske, C. Carreras, and D. Weinstein, Natural History of Hepatocellular Adenoma Formation in Glycogen Storage Disease Type I, The Journal of Pediatrics, vol.159, issue.3, pp.442-446, 2011.
DOI : 10.1016/j.jpeds.2011.02.031

W. Yiu, Y. Lee, and W. Peng, Complete Normalization of Hepatic G6PC Deficiency in Murine Glycogen Storage Disease Type Ia Using Gene Therapy, Molecular Therapy, vol.18, issue.6, pp.1076-1084, 2010.
DOI : 10.1038/mt.2010.64

W. Yiu, C. Pan, and R. Ruef, Angiotensin mediates renal fibrosis in the nephropathy of glycogen storage disease type Ia, Kidney International, vol.73, issue.6, pp.716-723, 2008.
DOI : 10.1038/sj.ki.5002718