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Dernières publications
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Valentina Taglietti, Kaouthar Kefi, Lea Rivera, Oriane Bergiers, Nastasia Cardone, et al.. Thyroid-stimulating hormone receptor signaling restores skeletal muscle stem cell regeneration in rats with muscular dystrophy. Science Translational Medicine, 2023, 15 (685), ⟨10.1126/scitranslmed.add5275⟩. ⟨hal-04150315⟩
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A. Morin, Amalia Stantzou, Olga N. Petrova, John C.W. Hildyard, T. Tensorer, et al.. Dystrophin myonuclear domain restoration governs treatment efficacy in dystrophic muscle. Proceedings of the National Academy of Sciences of the United States of America, 2023, 120 (2), ⟨10.1073/pnas.2206324120⟩. ⟨hal-04122777⟩
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Valentina Taglietti, Kaouthar Kefi, Iwona Bronisz-Budzyńska, Busra Mirciloglu, Mathilde Rodrigues, et al.. Duchenne muscular dystrophy trajectory in R-DMDdel52 preclinical rat model identifies COMP as biomarker of fibrosis. Acta Neuropathologica Communications, 2022, 10 (1), ⟨10.1186/s40478-022-01355-2⟩. ⟨hal-03828280⟩
Chiffres clés
48
Publications avec texte intégral
Open Access
67 %
Mots clés
Dynamin 2
Molecular docking
Mitochondrial fission
Inbred mdx
Clinical trials
Male
Myogenesis
Gene expression
CaV subunits
DMO
Hepatocellular carcinoma
LKB1
Humans
Dystrophin-EGFP
Dystrophie Musculaire de Becker BMD
Cell Line
Multi exon skipping
Calcium Channels
Multi resolution modeling
Long noncoding RNA
Cultured
Liver
Invivo
BMD
MES
Dystrophin
Myotendinous junction
Muscular dystrophy
Cell Biology
Human Umbilical Vein Endothelial Cells
CaVβs
Centronuclear myopathy
Inhibitors
Base Sequence
Delivery
Duchenne muscular dystrophy
CTNNB1
Calcium
Hear
DMD
Duchenne muscular dystrophy DMD
Immunoglobulin Fc Fragments/pharmacology
Gene modifiers
Duchenne DMD dystrophy
Metabolism
Ex-vivo
Génomique
Homeostasis
Genomic
Animal/physiopathology
Dystrophie Musculaire de Duchenne DMD
Becker muscular dystrophy BMD Duchenne muscular dystrophy DMD miRNA nNOS
Knockout
Long QT
LncARN
Muscles/physiopathology
Muscle development
Modificateurs de gènes
Allele‐specific silencing therapy
Dystrophin central domain
Morphogenesis
Becker muscular dystrophy BMD
Cardiomyopathy
Autophagy
Dystrophine
Dystrophie musculaire de Becker
Muscle
Activin Receptors
Cachexia
Muscle Biology
Animals
Energy Metabolism/drug effects
Skeletal muscle
Cells
Exon skipping
Mice
Gene Expression Regulation/drug effects
Multiresolution modeling
Muscle Strength
Cell homeostasis
L-Type
LncRNA
Molecular Sequence Data
Becker BMD muscular dystrophy
Antisense oligonucleotides
Muscular Atrophy
Dystrophy
Mdx mouse
Epigenetics
DHPR α1S
NAD+
Inbred C57BL
NNOS
Becker muscular dystrophy
Muscular Dystrophy
MiARN
CD38
Diseases
Drp1
Cardiomyopathie